A rare case of adult pulmonary Langerhans' cell histiocytosis

Abstract

The most common organ affected in smokers is lungs. The usual presentations are obstructive airway disease, interstitial lung disease, and malignancy. Rarely, some individuals with specific genomic characteristics may develop pulmonary Langerhans' cell histiocytosis, which commonly presents as bilateral upper lobe predominant cystic lung disease. The main array of treatment is cessation of smoking.