Generalized smooth muscle hypertrophy.

Abstract

This report presents a twenty-year-old man with generalized digestive and urinary smooth muscle hypertrophy combined with somatic and sexual hypodevelopment. We could not find in the literature any report related to the disease of our patient. Congenital pyloric stenosis is the less rare obstructive syndrome due to smooth muscle hypertrophy. Morgagni described this syndrome in an adult patient, in the XVIII century (2). Pyloroplasty is the best treatment for this disease. Other congenital or acquired obstructive syndromes of the digestive system such as Chagas' aganglionosis and pseudo-obstruction of the small bowel are also important clinical and surgical challenges (1,3,4). Several obstructive illnesses due to smooth muscle dysfunction have been described. This report presents an apparently original syndrome urinary segmental obstruction following smooth muscle hypertrophy.