Madelung deformity in a child with Léri-Weill dyschondrosteosis

Abstract

Madelung’s deformity is a type of wrist abnormality due to premature closure of the distal radius physis. It can be associated with a wide spectrum of pathologies, and 2 main groups have been differentiated, true-Madelung and pseudo-Madelung deformity, the presence of Vickers ligament and/or an anomalous radiotriquetral ligament being features of the former. We present the case of a child with a bilateral Madelung deformity, in the context of a Léri-Weill syndrome.