Electrical storm following pregnancy in systemic scleroderma: A case report.

IF 1.7 4区医学 Q3 CARDIAC & CARDIOVASCULAR SYSTEMS Pace-Pacing and Clinical Electrophysiology Pub Date : 2024-07-01 Epub Date: 2023-12-12 DOI:10.1111/pace.14904

Zahra Emkanjoo, Samira Shirazi, Farzad Kamali, Hamid Pouraliakbar, Mahsa Nourani, Firouz Balavandi

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Abstract

Introduction: Systemic sclerosis (SSc) is a rare connective tissue disease characterized by immune dysfunction, vascular damage, and fibrosis affecting the skin and multiple internal organs, such as the cardiovascular and respiratory systems. In some women with preexisting SSc, pregnancy is associated with negative maternal outcomes. Tachyarrhythmia is a common clinical manifestation of cardiovascular damage in SSc patients. However, few studies have reported the use of catheter ablation and an implantable cardioverter defibrillator (ICD) in patients with SSc complicated by ventricular tachycardia (VT).

Case: A 19-year-old woman known case of SSc referred to our center with recurrent VT during pregnancy and after delivery. Two-dimensional Echocardiogram showed severe systolic dysfunction with a left ventricular ejection fraction (LVEF) of 30%. Considering, recurrent VT despite medical treatment and the progressive nature of systemic sclerosis radiofrequency catheter (RF) ablation and ICD implantation were performed.

Conclusion: We report a case of systemic sclerosis complicated by VT and left ventricular (LV) dysfunction during pregnancy that was successfully treated with RF ablation.

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系统性硬皮病患者妊娠后的电风暴：病例报告。

简介系统性硬化症（SSc）是一种罕见的结缔组织疾病，其特点是免疫功能障碍、血管损伤和纤维化，影响皮肤和多个内脏器官，如心血管和呼吸系统。在一些患有 SSc 的妇女中，怀孕会对母体产生不良影响。快速性心律失常是 SSc 患者心血管损伤的常见临床表现。然而，很少有研究报告称导管消融和植入式心律转复除颤器（ICD）用于并发室性心动过速（VT）的 SSc 患者：病例：一名已知患有梭状红斑狼疮的 19 岁女性，因在怀孕期间和分娩后反复出现室性心动过速而转诊至本中心。二维超声心动图显示左心室射血分数（LVEF）为30%，存在严重的收缩功能障碍。尽管接受了药物治疗，但VT仍反复发作，考虑到系统性硬化症的进展性，我们对患者进行了射频导管（RF）消融术和ICD植入术：我们报告了一例在妊娠期间并发 VT 和左心室（LV）功能障碍的全身性硬化症病例，该病例成功接受了射频消融治疗。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Pace-Pacing and Clinical Electrophysiology 医学-工程：生物医学

CiteScore

2.70

自引率

5.60%

发文量

209

审稿时长

2-4 weeks

期刊介绍： Pacing and Clinical Electrophysiology (PACE) is the foremost peer-reviewed journal in the field of pacing and implantable cardioversion defibrillation, publishing over 50% of all English language articles in its field, featuring original, review, and didactic papers, and case reports related to daily practice. Articles also include editorials, book reviews, Musings on humane topics relevant to medical practice, electrophysiology (EP) rounds, device rounds, and information concerning the quality of devices used in the practice of the specialty.

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