COLLAPSING GLOMERULOPATHY IN HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS

Figer Ishika R, Shinde Sweety V
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Abstract

Hemophagocytic lymphohistiocytosis (HLH) is a potentially fatal hyperinammatory syndrome due to abnormal immune process and multiorgan inltration by phagocytic histiocytes. Renal presentation is very rare. Collapsing glomerulopathy with underlying autoimmune disease leading to HLH is documented in the present case.
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嗜血细胞淋巴组织细胞增多症中的塌陷性肾小球病变
嗜血细胞淋巴组织细胞增生症(HLH)是一种潜在的致命性高ammatory 综合征,由异常免疫过程和吞噬组织细胞的多器官内ltration引起。肾脏表现非常罕见。在本病例中,塌陷性肾小球病与潜在的自身免疫性疾病导致了HLH。
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