A Rare Cause of Acute Abdomen in Children: Segmental Absence of the Intestinal Musculature, a Case Report and Literature Review

IF 0.4 4区 医学 Q4 SURGERY Indian Journal of Surgery Pub Date : 2024-02-14 DOI:10.1007/s12262-024-04052-7
{"title":"A Rare Cause of Acute Abdomen in Children: Segmental Absence of the Intestinal Musculature, a Case Report and Literature Review","authors":"","doi":"10.1007/s12262-024-04052-7","DOIUrl":null,"url":null,"abstract":"<h3>Abstract</h3> <p>Segmental absence of the intestinal musculature (SAIM) is a rare clinicopathological entity in childhood. The etiology of SAIM has not been fully elucidated. Cases of SAIM are mostly documented in neonate and adult population. A 10-year-old girl was admitted to our clinic with the complaint of acute abdominal pain that was not relieved on medical management. Ultrasound abdomen showed diffuse thickening of duodenum, jejunum, and transverse colon wall. There was fluid collection in the left lower abdomen. In view of unrelieved abdominal distention, acute abdominal pain, and intestinal obstruction, a midline laparotomy was performed. Fibrous bands were compressing the jejunum with a small jejunum segment that appeared ischemic and was resected. Histopathological examination of this jejunum segment was reported as SAIM—a clear cut histopathological picture of mucosa and sub-mucosa with no muscularis propria was seen.</p>","PeriodicalId":13391,"journal":{"name":"Indian Journal of Surgery","volume":null,"pages":null},"PeriodicalIF":0.4000,"publicationDate":"2024-02-14","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Indian Journal of Surgery","FirstCategoryId":"3","ListUrlMain":"https://doi.org/10.1007/s12262-024-04052-7","RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q4","JCRName":"SURGERY","Score":null,"Total":0}
引用次数: 0

Abstract

Segmental absence of the intestinal musculature (SAIM) is a rare clinicopathological entity in childhood. The etiology of SAIM has not been fully elucidated. Cases of SAIM are mostly documented in neonate and adult population. A 10-year-old girl was admitted to our clinic with the complaint of acute abdominal pain that was not relieved on medical management. Ultrasound abdomen showed diffuse thickening of duodenum, jejunum, and transverse colon wall. There was fluid collection in the left lower abdomen. In view of unrelieved abdominal distention, acute abdominal pain, and intestinal obstruction, a midline laparotomy was performed. Fibrous bands were compressing the jejunum with a small jejunum segment that appeared ischemic and was resected. Histopathological examination of this jejunum segment was reported as SAIM—a clear cut histopathological picture of mucosa and sub-mucosa with no muscularis propria was seen.

查看原文
分享 分享
微信好友 朋友圈 QQ好友 复制链接
本刊更多论文
儿童急性腹部的罕见病因:肠道肌肉节段性缺失,病例报告和文献综述
摘要 节段性肠肌缺失(SAIM)是一种罕见的儿童临床病理现象。SAIM 的病因尚未完全阐明。SAIM病例多见于新生儿和成人。本诊所收治了一名 10 岁女孩,主诉为急性腹痛,经药物治疗后症状仍未缓解。腹部超声波检查显示十二指肠、空肠和横结肠壁弥漫性增厚。左下腹有积液。鉴于腹胀无法缓解、急性腹痛和肠梗阻,医生对患者进行了中线开腹手术。纤维带压迫了空肠,其中一小段空肠出现缺血并被切除。该段空肠的组织病理学检查报告为 SAIM--粘膜和粘膜下组织病理学图像清晰,未见固有肌。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
求助全文
约1分钟内获得全文 去求助
来源期刊
CiteScore
0.60
自引率
25.00%
发文量
412
审稿时长
6-12 weeks
期刊介绍: The Indian Journal of Surgery is the official publication of the Association of Surgeons of India that considers for publication articles in all fields of surgery. Issues are published bimonthly in the months of February, April, June, August, October and December. The journal publishes Original article, Point of technique, Review article, Case report, Letter to editor, Teachers and surgeons from the past - A short (up to 500 words) bio sketch of a revered teacher or surgeon whom you hold in esteem and Images in surgery, surgical pathology, and surgical radiology. A trusted resource for peer-reviewed coverage of all types of surgery Provides a forum for surgeons in India and abroad to exchange ideas and advance the art of surgery The official publication of the Association of Surgeons of India 92% of authors who answered a survey reported that they would definitely publish or probably publish in the journal again The Indian Journal of Surgery offers peer-reviewed coverage of all types of surgery. The Journal publishes Original articles, Points of technique, Review articles, Case reports, Letters, Images and brief biographies of influential teachers and surgeons. The Journal spans General Surgery, Pediatric Surgery, Neurosurgery, Plastic Surgery, Cardiothoracic Surgery, Vascular Surgery, Rural Surgery, Orthopedic Surgery, Urology, Surgical Oncology, Radiology, Anaesthesia, Trauma Services, Minimal Access Surgery, Endocrine Surgery, GI Surgery, ENT, Colorectal Surgery, surgical practice and research. The Journal provides a forum for surgeons from India and abroad to exchange ideas, to propagate the advancement of science and the art of surgery and to promote friendship among surgeons in India and abroad. This has been a trusted platform for surgons in communicating up-to-date scientific informeation to the community.
期刊最新文献
‘Mid-term Reflections of the President’—Charting Progress and Future Directions for the Association of Surgeons of India Clinico-Radiological Features of Acute and Chronic Superior Mesenteric Artery Occlusion (SMAO) Utilizing Hysteroscopic Mesh Resection for Presacral Mesh Infection Following Sacrocolpopexy Bleeding Jejunal Diverticula: Always a Timely Reminder Execution of Ipsilateral Radical Tonsillectomy and Tongue Base Mucosal Wedge Biopsy with Trans Oral Robotic Surgery (TORS) in the Setting of Carcinoma Unknown Primary (CUP): Insights into Surgical Techniques and Instrumentation
×
引用
GB/T 7714-2015
复制
MLA
复制
APA
复制
导出至
BibTeX EndNote RefMan NoteFirst NoteExpress
×
×
提示
您的信息不完整,为了账户安全,请先补充。
现在去补充
×
提示
您因"违规操作"
具体请查看互助需知
我知道了
×
提示
现在去查看 取消
×
提示
确定
0
微信
客服QQ
Book学术公众号 扫码关注我们
反馈
×
意见反馈
请填写您的意见或建议
请填写您的手机或邮箱
已复制链接
已复制链接
快去分享给好友吧!
我知道了
×
扫码分享
扫码分享
Book学术官方微信
Book学术文献互助
Book学术文献互助群
群 号:481959085
Book学术
文献互助 智能选刊 最新文献 互助须知 联系我们:info@booksci.cn
Book学术提供免费学术资源搜索服务,方便国内外学者检索中英文文献。致力于提供最便捷和优质的服务体验。
Copyright © 2023 Book学术 All rights reserved.
ghs 京公网安备 11010802042870号 京ICP备2023020795号-1