Francesca Piccinini, Mario Borgione, Giuseppe Riva, Giancarlo Pecorari
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引用次数: 0
Abstract
Introduction: Atypical pleomorphic adenoma (PA) is an uncommon tumor, more frequent in submandibular and parotid glands. PA is classified as atypical when it presents hypercellularity, necrosis or hyalinization, dysplasia, capsular violation or distant metastases.
Case report: We described a case of a 39-year-old female presented with a slowly growing mass involving the soft palate. A life-threatening bleeding from PA with hemorrhagic shock occurred and required ligation of the external carotid artery with tracheotomy. A transoral en-bloc excision of the mass (70 x 50 x 40 mm) was performed. Pathological exam demonstrated an atypical PA, with hypercellular fields and myoepithelial and squamous differentiation.
Conclusion: An appropriate diagnostic evaluation and a prompt intervention are essential to avoid dangerous complications, even for benign neoplasms.
导言:非典型多形性腺瘤(PA)是一种不常见的肿瘤,多发于颌下腺和腮腺。当PA出现高细胞性、坏死或透明化、发育不良、囊侵犯或远处转移时,就会被归类为非典型多形性腺瘤:我们描述了一例 39 岁女性的病例,她的软腭肿块生长缓慢。PA大出血并伴有失血性休克,危及生命,需要结扎颈外动脉并进行气管切开。手术对肿块(70 x 50 x 40 毫米)进行了经口全切。病理检查显示为非典型PA,有高细胞野、肌上皮和鳞状分化:结论:要避免危险的并发症,即使是良性肿瘤,也必须进行适当的诊断评估和及时干预。