A Case Report on the Short-Term Recurrence of Low-Grade Fibromyxoid Sarcoma in the Maxillary Sinus.

Dan Zhao, Jian Dai, Yu Hu, Tao Wang
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Abstract

Low-grade fibromyxoid sarcoma (LGFMS) represents an exceptionally rare soft-tissue tumor, challenging to diagnose, and notorious for relentless recurrence and proliferation postsurgical resection. Primary symptoms of LGFMS include nasal congestion and rhinorrhea, accompanied by cheek numbness and distension. In this article, we report the diagnosis and treatment of a case of low-grade LGFMS originating in the maxillary sinus (MS). A 64-year-old male diagnosed with LGFMS of the left MS, undergoing 3 surgeries over a 1-year period with subsequent local recurrence. Following inconclusive postoperative pathology after the initial surgery, the patient experienced recurrence 2 months postsurgery, necessitating a second operation, which confirmed the LGFMS diagnosis pathologically. Radiation therapy commenced 1 month after the second surgery; however, recurrence transpired 6 months later, leading to a third operation. Subsequently, recurrence occurred again 8 months post third surgery, with the patient currently undergoing targeted therapy. This case underscores the distinct characteristics and therapeutic challenges inherent in LGFMS through the narrative of diagnosis and progression of LGFMS originating in the MS.

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上颌窦低级别纤维肉瘤短期复发病例报告
低分化纤维肉瘤(LGFMS)是一种异常罕见的软组织肿瘤,诊断困难,手术切除后会不断复发和增生。LGFMS 的主要症状包括鼻塞和鼻出血,伴有面颊麻木和胀痛。本文报告了一例起源于上颌窦(MS)的低级别 LGFMS 的诊断和治疗。一名 64 岁的男性被诊断为左侧上颌窦 LGFMS,在 1 年内接受了 3 次手术,随后局部复发。首次手术后,术后病理结果不确定,患者术后2个月复发,不得不进行第二次手术,病理结果证实了LGFMS的诊断。第二次手术后 1 个月开始接受放射治疗,但 6 个月后复发,不得不进行第三次手术。第三次手术后 8 个月再次复发,目前患者正在接受靶向治疗。本病例通过叙述源于多发性硬化症的 LGFMS 的诊断和进展,强调了 LGFMS 的独特特征和固有的治疗挑战。
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