Juvenile psammomatoid cemeto-ossifying fibroma: Two cases

Abstract

Juvenile ossifying fibroma is a variant of ossifying fibroma, commonly involving sinunasal tract of children. It is an aggressive condition that leads to the destruction of adjacent structures. Distinction from other fibro-osseous lesions is important. Juvenile ossifying fibroma has two histologic subtypes that are psammomatous and trabecular type. We present herein two cases of juvenile psammomatoid ossifying fibroma occuring in a 22 month old and a 5 year old child, which arose in the bilateral maxillary sinuses and led to bulging of the cheek and nasal obstruction. The tumor in case 1 could not be completely excised due to its huge size and massive destruction of the bilateral maxilla. The tumor in case 2 was completely excised through staged operations. Tumors in both cases were diagnosed as juvenile pammomatoid cement-ossifying fibroma by the histology. Here, we report two cases from Korea and describe psammomatoid morphology and how to differentiate it from other fibro-osseous lesions.