{"title":"[青少年皮肌炎疾病评估进展]。","authors":"L Sun, X M Tang","doi":"10.3760/cma.j.cn112140-20221108-00952","DOIUrl":null,"url":null,"abstract":"幼年型皮肌炎(JDM)是儿童期罕见的自身免疫性炎症性肌炎,特征为皮肤和横纹肌的非化脓性炎症,临床表现为特征性皮疹、近端肌无力及肌酶升高,JDM可累及其他内脏器官系统,突出影响胃肠道和呼吸系统,严重者出现呼吸衰竭需重症监护管理。对JDM患儿的管理需要定期评估疾病活动度和脏器损伤程度以及通过标准化的测量工具评估治疗反应。本文总结了国内外常用的JDM病情评估方法,对评估工具的内容、特点、应用情况等进行综述,为临床医师进行JDM病情评估、指导治疗及预后提供参考依据。.","PeriodicalId":23998,"journal":{"name":"Zhonghua er ke za zhi = Chinese journal of pediatrics","volume":null,"pages":null},"PeriodicalIF":0.0000,"publicationDate":"2023-06-02","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"[Disease assessment progress of juvenile dermatomyositis].\",\"authors\":\"L Sun, X M Tang\",\"doi\":\"10.3760/cma.j.cn112140-20221108-00952\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"幼年型皮肌炎(JDM)是儿童期罕见的自身免疫性炎症性肌炎,特征为皮肤和横纹肌的非化脓性炎症,临床表现为特征性皮疹、近端肌无力及肌酶升高,JDM可累及其他内脏器官系统,突出影响胃肠道和呼吸系统,严重者出现呼吸衰竭需重症监护管理。对JDM患儿的管理需要定期评估疾病活动度和脏器损伤程度以及通过标准化的测量工具评估治疗反应。本文总结了国内外常用的JDM病情评估方法,对评估工具的内容、特点、应用情况等进行综述,为临床医师进行JDM病情评估、指导治疗及预后提供参考依据。.\",\"PeriodicalId\":23998,\"journal\":{\"name\":\"Zhonghua er ke za zhi = Chinese journal of pediatrics\",\"volume\":null,\"pages\":null},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2023-06-02\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Zhonghua er ke za zhi = Chinese journal of pediatrics\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.3760/cma.j.cn112140-20221108-00952\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Zhonghua er ke za zhi = Chinese journal of pediatrics","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.3760/cma.j.cn112140-20221108-00952","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}