【1例胆固醇酯储存病肝脏形态及临床观察】。

Deutsche Zeitschrift fur Verdauungs- und Stoffwechselkrankheiten Pub Date : 1988-01-01

J Justus, J Schulze, C Kemmer, H Riedel

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引用次数: 0

摘要

本文报告1例胆固醇酯储存病的肝脏标本形态及临床病程。在一个16岁的男孩的第一次活检中，光镜下发现大量的中性脂肪储存，显微极化下发现胆固醇酯。晚期门脉野纤维化和严重的反应性肝炎表明进展到化生的危险。电镜下可见肝细胞、星状细胞及胆管上皮中典型的膜包裹性脂质包涵体。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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[Liver morphology and clinical aspects of a case of cholesterol ester storage disease].

Liver specimen morphology and clinical course of a case of cholesterol ester storage disease are presented. In a 16-year-old boy on the first biopsy a massive storage of neutral fats was found light microscopically and of cholesterol ester micropolariscopically. Advanced portal field fibrosis and severe reactive hepatitis indicate the danger of progression up to metaplasia. Typical membrane-surrounded lipid inclusions were found electron microscopically in hepatic cells, stellate cells and also in bile duct epithelium.

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Deutsche Zeitschrift fur Verdauungs- und Stoffwechselkrankheiten

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