毛发综合征患者使用超纳米填充树脂进行上前区口腔美学修复:病例报告。

IF 0.9 Q3 DENTISTRY, ORAL SURGERY & MEDICINE Special Care in Dentistry Pub Date : 2024-07-01 Epub Date: 2024-02-20 DOI:10.1111/scd.12979
Patricia Nataly Conto Quispe, Akemy Celeste Tapia Martinez, Henry Jesús Vilcapoma Guerra, Lenny Lavado García, Gilmer Torres Ramos
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引用次数: 0

摘要

背景介绍毛发综合症(WHS)是一种罕见的先天性疾病,会影响非黑人的毛发结构。其发病机制尚未明确。据推测,毛囊中的脱绒毛体(特别是脱绒毛素、胎盘蛋白和胎盘素-1,它们是细胞结构蛋白,可保持紧密细胞间的粘附性)在这种病症中会发生改变,导致细胞结合脆弱。这种病症又可细分为两大类:局部或环状变异型和全身变异型。从出生或出生后的头几个月开始,WHS 患者的临床特征就是部分或整个头皮出现非常短的卷曲头发,通常直径较小、质地较脆、颜色较浅。最常见的皮肤表现是毛囊角化症和掌跖角化症。诊断以临床表现为基础,并通过毛发镜检查加以辅助。然而,WHS 的确诊需要进行基因检测。可能会出现口腔发育不全、釉质缺损(如矿化不足)、非典型龋、牙包涵体和畸形针状牙:临床病例:利马布雷尼亚国家儿童健康研究所(NIHCH:Breña, Lima)的一名 5 岁女性患者被诊断患有 WHS,该患者由遗传科转诊至儿童牙科,以筛查与牙源性感染和牙齿畸形相关的爆发性感染。在口腔外窥镜检查中,发现患者毛细血管长度短、头发脆而卷、皮肤干燥、指甲营养不良。口腔内临床检查发现,所有牙齿都有前牙52、51、61、62和釉质矿化不足。放射检查显示,41、34 和 45 号牙齿部分缺失。由于病例复杂,牙科综合治疗在手术室全身麻醉下进行。作为替代治疗方法,建议对 52、51、61 和 62 号牙进行牙槽骨切除术,植入复合树脂,并采用模拟技术用超微纳米填充树脂进行修复:结论:使用模拟技术制作超纳米填充树脂牙冠,是对 WHS 患者乳牙进行口腔美学修复的一种替代治疗方法。使用超纳米填充树脂实现了美学治疗。经过 12 个月的牙科治疗后,患者的咀嚼、发音和美观都得到了改善。
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Aesthetic oral rehabilitation of the upper-anterior sector with supra-nano filling resin in a patient with woolly hair syndrome: case report.

Background: Woolly Hair Syndrome (WHS) is a rare birth condition that affects the structure of hair in non-black people. The pathogenesis is not yet defined. It is postulated that the hair follicle's desmosomes (specifically desmoplaquine, placoglobin and placofilin-1, which are cell structural proteins that keep the adhesion among close cells) would be altered in this pathology, leading to fragility in the cellular union. It is subdivided into two large groups: the localized or circumscribed variant and the generalized variant. From birth or first months of life, patients with WHS are clinically characterized by the presence of a portion or entire scalp area of very short frizzy hair, usually of a smaller diameter, brittle and lighter color. The most frequent skin manifestations are pilar keratosis and palmo-plantar keratodermia. The diagnosis is based on the clinical findings, and it is facilitated by trichotoscopic examination. However, a definitive diagnosis of WHS requires genetic testing. Oral agenesis, enamel defects (such as hypomineralization), atypical caries, dental inclusion, and malformed pin-shaped teeth may occur.

Objective: To describe an aesthetic alternative of oral rehabilitation using the mock-up technique in a patient with WHS.

Clinical case: A 5-year-old female patient diagnosed with WHS from the National Institute of Child Health NIHCH: Breña, Lima, who was referred from the Genetic service to the Pediatric Dentistry service in order to screen outbreaks of infection associated with odontogenic origin and dental anomalies. At the ectoscopy, a patient with short capillary length, brittle and curly hair, dry skin, and nail dystrophy was observed. At the intraoral clinical examination, anterior pieces of 52, 51, 61, 62, and enamel hypomineralization were observed in all teeth. The radiographic examination showed agenesis of parts 41, 34, and 45. Integral dental treatment was performed in the operating room under general anesthesia due to the complexity of the case. Pulpectomy in pieces 52, 51, 61, 62, post of composite resin, and rehabilitation with supra-nanow filling resin using the mock-up technique were proposed as alternative treatments.

Conclusion: The making of supra-nano filling resin-based crowns using the mock-up technique is an alternative treatment for aesthetic oral rehabilitation in deciduous dentition of patients with WHS. The aesthetic treatment was achieved using supra nano-filling resins. After 12 months of dental treatment, a favorable response was observed, improving the chewing, phonation and aesthetics of the patient.

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来源期刊
Special Care in Dentistry
Special Care in Dentistry DENTISTRY, ORAL SURGERY & MEDICINE-
CiteScore
2.40
自引率
14.30%
发文量
120
期刊介绍: Special Care in Dentistry is the official journal of the Special Care Dentistry Association, the American Association of Hospital Dentists, the Academy of Dentistry for Persons with Disabilities, and the American Society for Geriatric Dentistry. It is the only journal published in North America devoted to improving oral health in people with special needs.
期刊最新文献
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