成人塑料支气管炎:慢性癌性咳嗽的罕见病因

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引用次数: 0

摘要

塑性支气管炎是一种发病率很高的罕见疾病。我们报告了一例 48 岁的男性吸烟者,其既往病史包括糖尿病、肺气肿、反复呼吸道感染、恶化的有痰咳嗽以及过去 3 个月中氧气需求量的增加。塑性支气管炎常出现在儿童群体中,因此在考虑慢性痰液分泌不畅的肺部疾病时,必须将其列入鉴别诊断范围。组织学上的脂质浸润具有诊断意义,通常需要进行外科活检以进行充分的组织分析。淋巴管造影既可用于确诊,也可用于治疗,这取决于是否有机构提供图像引导下的选择性淋巴管栓塞治疗。
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Adult Plastic Bronchitis: A Rare Cause for Chronic Productive Cough

Plastic bronchitis is a rare disease with serious morbidity. We report a case of a 48-year-old male smoker with a past medical history of diabetes, emphysema, recurrent respiratory infections, a worsening productive cough, and increased oxygen requirement over the past 3 months. Often described in the pediatric population, it is important to maintain plastic bronchitis in the differential when considering unresolving pulmonary conditions with chronic sputum production. Lipid infiltration on histology is diagnostic and often requires surgical biopsy for adequate tissue analysis. A lymphangiogram can be both confirmatory and therapeutic depending on the institutional availability of image-guided selective lymphatic embolization.

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