Ramyasree Bade, N. Peters, Joseph L Mathew, I. Sen, J. K. Mahajan
{"title":"可通过手术矫正的中枢性青紫症:一名儿童的先天性肝外门静脉分流术","authors":"Ramyasree Bade, N. Peters, Joseph L Mathew, I. Sen, J. K. Mahajan","doi":"10.4103/jiaps.jiaps_1_24","DOIUrl":null,"url":null,"abstract":"ABSTRACT\n \n Congenital extrahepatic portosystemic shunts (CEPS) are rare anomalies connecting the portal system to the inferior vena cava. This report discusses a 10-year-old boy with Type II c CEPS, presenting cyanosis and dyspnea. Surgical ligation resulted in significant improvement in symptoms. Early identification and intervention are crucial, necessitating a protocolized approach.","PeriodicalId":16069,"journal":{"name":"Journal of Indian Association of Pediatric Surgeons","volume":"11 3","pages":""},"PeriodicalIF":0.0000,"publicationDate":"2024-07-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Surgically Correctable Central Cyanosis: Congenital Extrahepatic Portosystemic Shunt in a Child\",\"authors\":\"Ramyasree Bade, N. Peters, Joseph L Mathew, I. Sen, J. K. Mahajan\",\"doi\":\"10.4103/jiaps.jiaps_1_24\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"ABSTRACT\\n \\n Congenital extrahepatic portosystemic shunts (CEPS) are rare anomalies connecting the portal system to the inferior vena cava. This report discusses a 10-year-old boy with Type II c CEPS, presenting cyanosis and dyspnea. Surgical ligation resulted in significant improvement in symptoms. Early identification and intervention are crucial, necessitating a protocolized approach.\",\"PeriodicalId\":16069,\"journal\":{\"name\":\"Journal of Indian Association of Pediatric Surgeons\",\"volume\":\"11 3\",\"pages\":\"\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2024-07-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Journal of Indian Association of Pediatric Surgeons\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.4103/jiaps.jiaps_1_24\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"Q3\",\"JCRName\":\"Medicine\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Journal of Indian Association of Pediatric Surgeons","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.4103/jiaps.jiaps_1_24","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q3","JCRName":"Medicine","Score":null,"Total":0}
引用次数: 0
摘要
摘要 先天性肝外门静脉分流(CEPS)是连接门静脉系统和下腔静脉的罕见畸形。本报告讨论了一名患有 II c 型 CEPS 的 10 岁男孩,他出现发绀和呼吸困难。手术结扎后症状明显改善。早期识别和干预至关重要,因此必须采用规范化的方法。
Surgically Correctable Central Cyanosis: Congenital Extrahepatic Portosystemic Shunt in a Child
ABSTRACT
Congenital extrahepatic portosystemic shunts (CEPS) are rare anomalies connecting the portal system to the inferior vena cava. This report discusses a 10-year-old boy with Type II c CEPS, presenting cyanosis and dyspnea. Surgical ligation resulted in significant improvement in symptoms. Early identification and intervention are crucial, necessitating a protocolized approach.
期刊介绍:
Journal of Indian Association of Pediatric Surgeons is the official organ of Indian Association of Pediatric Surgeons. The journal started its journey in October 1995 under the Editor-in-Chief Prof. Subir K Chatterjee. An advisory board was formed with well-versed internationally reputed senior members of our society like Late Prof. R K Gandhi, Prof. I C Pathak, Prof. P Upadhyay, Prof. T Dorairajan and many more. since then the journal is published quarterly uninterrupted. The journal publishes original articles, case reports, review articles and technical innovations. Special issues on different subjects are published every year. There have been several contributions from overseas experts.