非压实性心肌病和妊娠:一个令人担忧的共存结局。

Experimental & Clinical Cardiology Pub Date : 2012-09-01
Sotiris C Plastiras, Constantinos Pamboucas, Savvas Toumanidis
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引用次数: 0

摘要

在过去的25年里,左心室心肌不致密性得到了越来越多的认识。这种罕见的疾病是由心肌形态发生停止引起的。典型的三重并发症是心力衰竭、心律失常(包括心源性猝死)和全身栓塞事件。关于女性左室非压实性心肌病和妊娠结局的资料缺乏。第一次报告平安无事阴道分娩没有恶化的左心室非压实性心肌病是提出的。
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Noncompaction cardiomyopathy and pregnancy: An alarming coexistence ending in a favourable outcome.

Noncompaction of the left ventricular myocardium has gained increasing recognition over the past 25 years. This rare disease is caused by the arrest of myocardial morphogenesis. The classical triad of complications are heart failure, arrhythmias, including sudden cardiac death, and systemic embolic events. There is a paucity of data regarding women with left ventricular noncompaction cardiomyopathy and pregnancy outcome. The first report of an uneventful vaginal delivery without deterioration of left ventircular noncompaction cardiomyopathy is presented.

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来源期刊
Experimental & Clinical Cardiology
Experimental & Clinical Cardiology CARDIAC & CARDIOVASCULAR SYSTEMS-
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审稿时长
6-12 weeks
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