{"title":"淋巴管造影治疗顽固性先天性乳糜胸(附2例报告)","authors":"Naoya Kinota, Hiroshi Kodama, Taiki Moriyama, Junichi Taniguchi, Mitsunari Maruyama, Atsushi Ogasawara, Yasukazu Kako, Kaoru Kobayashi, Haruyuki Takaki, Akio Shibata, Kyoko Minagawa, Yasuhiro Takeshima, Koichiro Yamakado","doi":"10.22575/interventionalradiology.2021-0014","DOIUrl":null,"url":null,"abstract":"<p><p>In this study, we report two cases in which intranodal lymphangiography helped improve congenital chylothorax due to RASopathies. We performed lymphangiography after conservative treatments failed to improve chylothorax in an 8-year-old girl with cardiofaciocutaneous syndrome and a 2-month-old boy with Noonan syndrome. Inguinal lymph nodes were punctured with 25-gauge needles under ultrasonographic guidance, and 4 and 1 mL of iodized oil were injected, respectively, showing a backflow of iodized oil into the lungs. Chylothorax had improved in both patients after nodal lymphangiography. However, the second child experienced worsening of disease-associated extremity edema and died of sepsis 4 months later.</p>","PeriodicalId":73503,"journal":{"name":"Interventional radiology (Higashimatsuyama-shi (Japan)","volume":"7 1","pages":"17-20"},"PeriodicalIF":0.0000,"publicationDate":"2022-01-12","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://ftp.ncbi.nlm.nih.gov/pub/pmc/oa_pdf/ed/83/2432-0935-7-1-0017.PMC9327383.pdf","citationCount":"0","resultStr":"{\"title\":\"Lymphangiography as a Treatment for Refractory Congenital Chylothorax Due to RASopathies: A Report of Two Cases.\",\"authors\":\"Naoya Kinota, Hiroshi Kodama, Taiki Moriyama, Junichi Taniguchi, Mitsunari Maruyama, Atsushi Ogasawara, Yasukazu Kako, Kaoru Kobayashi, Haruyuki Takaki, Akio Shibata, Kyoko Minagawa, Yasuhiro Takeshima, Koichiro Yamakado\",\"doi\":\"10.22575/interventionalradiology.2021-0014\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>In this study, we report two cases in which intranodal lymphangiography helped improve congenital chylothorax due to RASopathies. We performed lymphangiography after conservative treatments failed to improve chylothorax in an 8-year-old girl with cardiofaciocutaneous syndrome and a 2-month-old boy with Noonan syndrome. Inguinal lymph nodes were punctured with 25-gauge needles under ultrasonographic guidance, and 4 and 1 mL of iodized oil were injected, respectively, showing a backflow of iodized oil into the lungs. Chylothorax had improved in both patients after nodal lymphangiography. However, the second child experienced worsening of disease-associated extremity edema and died of sepsis 4 months later.</p>\",\"PeriodicalId\":73503,\"journal\":{\"name\":\"Interventional radiology (Higashimatsuyama-shi (Japan)\",\"volume\":\"7 1\",\"pages\":\"17-20\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2022-01-12\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://ftp.ncbi.nlm.nih.gov/pub/pmc/oa_pdf/ed/83/2432-0935-7-1-0017.PMC9327383.pdf\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Interventional radiology (Higashimatsuyama-shi (Japan)\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.22575/interventionalradiology.2021-0014\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"2022/3/1 0:00:00\",\"PubModel\":\"eCollection\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Interventional radiology (Higashimatsuyama-shi (Japan)","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.22575/interventionalradiology.2021-0014","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2022/3/1 0:00:00","PubModel":"eCollection","JCR":"","JCRName":"","Score":null,"Total":0}
Lymphangiography as a Treatment for Refractory Congenital Chylothorax Due to RASopathies: A Report of Two Cases.
In this study, we report two cases in which intranodal lymphangiography helped improve congenital chylothorax due to RASopathies. We performed lymphangiography after conservative treatments failed to improve chylothorax in an 8-year-old girl with cardiofaciocutaneous syndrome and a 2-month-old boy with Noonan syndrome. Inguinal lymph nodes were punctured with 25-gauge needles under ultrasonographic guidance, and 4 and 1 mL of iodized oil were injected, respectively, showing a backflow of iodized oil into the lungs. Chylothorax had improved in both patients after nodal lymphangiography. However, the second child experienced worsening of disease-associated extremity edema and died of sepsis 4 months later.
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