原发性中枢神经系统脉管炎的治疗

IF 1.3 4区 医学 Q4 NEUROIMAGING Neuroimaging Clinics of North America Pub Date : 2023-08-21 DOI:10.1016/j.nic.2023.07.008
Alison M. Bays MD, MPH&TM
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引用次数: 0

摘要

原发性中枢神经系统血管炎(PCNSV)是一种局限于脑和脊髓的血管炎。诱导治疗通常由类固醇和环磷酰胺组成。维持治疗包括泼尼松逐渐减少,并可与硫唑嘌呤或霉酚酸酯等药物联合使用。复发在PCNSV中很常见,通常会增加类固醇剂量,有时会改变治疗方法。对于那些最初治疗无效或疾病复发的患者,利妥昔单抗和霉酚酸酯等药物可能是很好的选择。文献报道的死亡率为8%至9%。
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Treatment of Primary Angiitis of the Central Nervous System
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来源期刊
CiteScore
4.10
自引率
0.00%
发文量
89
审稿时长
>12 weeks
期刊介绍: Published four times a year—February, May, August, and November—Neuroimaging Clinics of North America updates you on the latest trends in patient management, keeps you up to date on the newest advances, and provides a sound basis for choosing treatment options. Each issue focuses on a single topic in neuroimaging and is presented under the direction of an experienced editor. Topics include brain and spine, head and neck, vascular, nerves, pediatric, movement disorders, and dementia. In addition, you can also purchase a CME subscription that offers up to 60 AMA Category 1 credits per year.
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