一例多发性骨髓瘤的组织浆细胞感染作为诊断难题

IF 0.8 Q4 ONCOLOGY South Asian Journal of Cancer Pub Date : 2023-06-09 eCollection Date: 2025-07-01 DOI:10.1055/s-0043-1761279
Manasi C Mundada, Faiq Ahmed, Bharat Potturu, Pavan Kumar
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引用次数: 0

摘要

组织原体是环境中常见的二形态真菌。这种真菌在免疫活性宿主中感染可能会出现流感样症状,也可能是无害的。然而,在免疫功能低下的宿主中,它可以引起任何临床亚型:肺部疾病、播散性疾病或全身性疾病。1本文报告一例多发性骨髓瘤患者,在同种异体骨髓移植后出现播散性组织胞浆菌病。一位45岁的绅士,已知患有肺结核,背部疼痛。患者接受了完整疗程的ATT。骨髓检查显示80%的浆细胞。电泳显示存在M带,免疫组化研究证明其为IgGκ亚型。血清游离轻链比例紊乱。患者接受了硼替佐米、来那度胺和地塞米松的诱导化疗;然而,它并没有完全缓解,因此建议他进行自体干细胞移植。他接受了干细胞移植,并接受了8个月的依那利胺治疗。然而,他的病情在10个月后复发,他开始服用4毫克的泊马度胺和6个周期的地塞米松,然后服用2毫克的单剂泊马度酰胺,并进行随访。目前,移植后3.5年,患者出现持续性血小板减少症。骨髓显示骨髓细胞增生,环钻活检显示单个肉芽肿,由少数组织细胞和单个巨细胞组成。PAS和GMS染色
本文章由计算机程序翻译,如有差异,请以英文原文为准。

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1.00
自引率
0.00%
发文量
80
审稿时长
35 weeks
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