Pilomatrix carcinoma in the presternal region. Very rare or very often misdiagnosed malignancy?

Pilomatrix carcinoma is a very rarely diagnosed malignancy. There are around 150 cases reported in the literature. In the very past this type of carcinoma was considered as a low-grade, non-metastasizing tumor. Nowadays with its high potential of recurrence and metastasizing the approach to this type of neoplasm should always be careful and multidisciplinary. The first line of therapy is wide surgical excision, followed by adjuvant radiotherapy. If there is observation of lymph node metastases they should be surgically or radiotherapeutically treated.  In the present case report, we present a 46-year-old patient with pilomatrix carcinoma in the presternal region.