AVAPS无创通气成功治疗Prader-Willi综合征患者呼吸衰竭。

IF 0.8 Q3 MEDICINE, GENERAL & INTERNAL Case Reports in Medicine Pub Date : 2023-01-01 DOI:10.1155/2023/9925144
Nauras Hwig, Montserrat Diaz-Abad, Victor T Peng, Jennifer Y So, Anayansi Lasso-Pirot
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引用次数: 1

摘要

普瑞德-威利综合征(PWS)是最常见的肥胖综合征,它开始于儿童早期的贪食症。由于肥胖的发展,这些患者中阻塞性睡眠呼吸暂停(OSA)的患病率很高。本病例报告提出了一例PWS合并病态肥胖、严重OSA和肥胖低通气综合征的患者,因低氧血症和高碳酸血症性呼吸衰竭入院。无创通气(NIV)与平均容量保证压力支持,一种较新的无创通气模式,成功地治疗了该患者,在住院期间和出院后的长期内均取得了重大的临床和气体交换改善。
本文章由计算机程序翻译,如有差异,请以英文原文为准。

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Successful Treatment of Respiratory Failure in a Patient with Prader-Willi Syndrome with Noninvasive Ventilation with AVAPS.

Prader-Willi syndrome (PWS) is the most prevalent syndromic form of obesity, which starts during early childhood in the setting of hyperphagia. Due to the development of obesity, there is a high prevalence of obstructive sleep apnea (OSA) among these patients. This case report presents a patient with PWS with morbid obesity, severe OSA, and obesity hypoventilation syndrome admitted to the hospital for hypoxemic and hypercapnic respiratory failure. Noninvasive ventilation (NIV) with average volume-assured pressure support, a newer NIV modality, was used successfully to treat this patient, achieving major clinical and gas exchange improvement both during the hospitalization and long term after discharge.

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来源期刊
Case Reports in Medicine
Case Reports in Medicine MEDICINE, GENERAL & INTERNAL-
CiteScore
1.70
自引率
0.00%
发文量
53
审稿时长
13 weeks
期刊最新文献
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