doge - potter综合征并发巨大腹部孤立性纤维性肿瘤1例报告及文献复习。

IF 1.6 4区 医学 Q2 Medicine Acta Clinica Belgica Pub Date : 2023-08-01 DOI:10.1080/17843286.2023.2165652
Joris Rötgens, Bruno Lapauw, Guy T'Sjoen
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引用次数: 1

摘要

一名63岁的男性早上出现意识减退症状腹部有巨大肿块来我们医院寻求第二意见。调查显示非糖尿病性低胰岛素性低血糖事件。切除腹部肿块解决了低血糖。解剖病理检查证实为孤立性纤维性肿瘤(SFT)。多吉-波特综合症被诊断出来。doge - potter综合征是一种潜在威胁生命的罕见副肿瘤综合征,其特征是由于孤立性纤维性肿瘤中胰岛素样生长因子- ii(促胰岛素样生长因子- ii)的激素前形式过量产生而导致复发性低胰岛素血症性低血糖。首先,我们描述病例的临床、实验室和放射学表现。其次,简要回顾了多吉-波特综合征的相关文献。
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Doege-Potter syndrome in a patient with a giant abdominal solitary fibrous tumor: a case report and review of the literature.

A 63-year-old man with spells of reduced consciousness in the morning and a giant abdominal mass presented to our institution for a second opinion. Investigation revealed non-diabetic hypoinsulinemic hypoglycemic events. Removal of the abdominal mass solved the hypoglycemia. Anatomopathological examination confirmed a solitary fibrous tumor (SFT). Doege-Potter syndrome was diagnosed. Doege-Potter syndrome is a potentially life-threatening rare paraneoplastic syndrome characterized by recurrent hypoinsulinemic hypoglycemia due to the overproduction of a prohormone form of insulin-like growth factor-II (pro-IGF-II) from a solitary fibrous tumor. First, we describe the clinical, laboratory and radiologic findings of the case. Second, a brief literature review on Doege-Potter syndrome is provided.

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来源期刊
Acta Clinica Belgica
Acta Clinica Belgica 医学-医学:内科
CiteScore
2.90
自引率
0.00%
发文量
44
审稿时长
6-12 weeks
期刊介绍: Acta Clinica Belgica: International Journal of Clinical and Laboratory Medicine primarily publishes papers on clinical medicine, clinical chemistry, pathology and molecular biology, provided they describe results which contribute to our understanding of clinical problems or describe new methods applicable to clinical investigation. Readership includes physicians, pathologists, pharmacists and physicians working in non-academic and academic hospitals, practicing internal medicine and its subspecialties.
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