{"title":"Autoinflammation and Myelofibrosis: Report of a Case","authors":"Prasad R. Koduri, Amina Shaik, Durga Rao Vegulada","doi":"10.4274/tjh.galenos.2023.2023.0064","DOIUrl":null,"url":null,"abstract":"Adult-onset Still’s disease (AOSD) is a rare systemic autoinflammatory disease of unknown etiology [1,2]. We describe the case of a young woman with AOSD who presented with extreme anemia and was diagnosed with secondary myelofibrosis. Treatment with prednisolone resulted in durable complete clinical and hematological response. She remains in excellent health, with normal blood counts over the course of 4 years of follow-up.","PeriodicalId":23362,"journal":{"name":"Turkish Journal of Hematology","volume":"40 3","pages":"223-224"},"PeriodicalIF":1.5000,"publicationDate":"2023-08-31","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://ftp.ncbi.nlm.nih.gov/pub/pmc/oa_pdf/9d/d8/TJH-40-223.PMC10476249.pdf","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Turkish Journal of Hematology","FirstCategoryId":"3","ListUrlMain":"https://doi.org/10.4274/tjh.galenos.2023.2023.0064","RegionNum":4,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2023/7/31 0:00:00","PubModel":"Epub","JCR":"Q3","JCRName":"HEMATOLOGY","Score":null,"Total":0}
引用次数: 0
Abstract
Adult-onset Still’s disease (AOSD) is a rare systemic autoinflammatory disease of unknown etiology [1,2]. We describe the case of a young woman with AOSD who presented with extreme anemia and was diagnosed with secondary myelofibrosis. Treatment with prednisolone resulted in durable complete clinical and hematological response. She remains in excellent health, with normal blood counts over the course of 4 years of follow-up.
期刊介绍:
The Turkish Journal of Hematology is published quarterly (March, June, September, and December) by the Turkish Society of Hematology. It is an independent, non-profit peer-reviewed international English-language periodical encompassing subjects relevant to hematology.
The Editorial Board of The Turkish Journal of Hematology adheres to the principles of the World Association of Medical Editors (WAME), International Council of Medical Journal Editors (ICMJE), Committee on Publication Ethics (COPE), Consolidated Standards of Reporting Trials (CONSORT) and Strengthening the Reporting of Observational Studies in Epidemiology (STROBE).
The aim of The Turkish Journal of Hematology is to publish original hematological research of the highest scientific quality and clinical relevance. Additionally, educational material, reviews on basic developments, editorial short notes, images in hematology, and letters from hematology specialists and clinicians covering their experience and comments on hematology and related medical fields as well as social subjects are published. As of December 2015, The Turkish Journal of Hematology does not accept case reports. Important new findings or data about interesting hematological cases may be submitted as a brief report.