Giant-Cell Fibroblastoma and Dermato Fibro Sarcoma Protuberans: The Same Tumoral Spectrum?

Abstract

We describe two cases of giant-cell fibroblastoma (GCF) with dermato fibro sarcoma protuberans (DFSP) component, occurring in two children in a chest wall localization. One case recurred 1 year fater. The two patients were tumor-free 12 and 8 years later. GCF is a rare mesenchymaf cutaneous and subcutaneous tumor reported mostly in the first two decades of life. Derrnato fibro sarcoma protuberans, occurring preferentially in adults, is a rare skin tumor with a pronounced tendency to local recurrence. Some cases of association of recurrence of GFC under the form of DFSP have been reported, raising the question of a continuum between the two tumors. The treatment of choice of the two tumors is a wide local excision.