Inflammatory Myofibroblastic Tumor: Encounter with A Rare Tumour in Pediatric Age Group

Abstract

Inflammatory myofibroblastic tumor, a rare benign tumor, occurs at any site in the body, is more common in pediatric age group than adult. Among them, inflammatory myofibroblastic tumors arising from stomach and mesentery are rare entity. We report two cases Barium swallow examination lower gastro-esophageal junction with bird-beak Endoscopy esophagus. During operation, the mass was found to be in fundus of stomach obstructing gastro-esophageal junction and total radical gastrectomy was done and histopathology report traced inflammatory myofibroblastic tumor. 7 years old boy presented with recurrent (two times operated) ill-defined, periumbilical abdominal mass. Previous tissue biopsy was non-conclusive. Abdominal Contrast CT Scan revealed heterogenous mass in epigastric and umbilical region encasing Superior Mesenteric Artery (SMA), which could not be separated from small bowel loops. During operation, the tumor was found to be arising from root of mesentery, encasing SMA & Head of Pancreas and adhere with almost middle ½ of small intestine. Debulking of mass along with resection anastomosis of small intestine was realized and histopathology report traced inflammatory myofibroblastic tumour. Keywords: