[NMR of phakomatoses].

Rivista di neurologia Pub Date : 1990-05-01
F Campodonico, R Guerrisi, V Guerrisi, G Brienza, R Floris
{"title":"[NMR of phakomatoses].","authors":"F Campodonico,&nbsp;R Guerrisi,&nbsp;V Guerrisi,&nbsp;G Brienza,&nbsp;R Floris","doi":"","DOIUrl":null,"url":null,"abstract":"<p><p>23 patients affected by phakomatoses were studied with NMR, including tuberous sclerosis (11 cases), Sturge-Weber's disease and Von Recklinghausen's neurofibromatosis (6 cases). SE sequence was used performing T1-WIs with TR = 350-750 ms and TE = 20-30 ms and T2-WIs with TR = 1500-2100 ms and TE = 50-100 ms. Tuberous sclerosis was characterized in each case by the presence of hiperintense areas in T2-WIOs, associated in 9 cases to subependimal microcalcifications. Sturge-Weber-disease showed: cerebral or lobar emiatrophia, abnormal vascularization and cortical calcifications. Cerebral neurofibromatosis was characterized by extra-assial tumors, associated in 4 cases to gliomas of the optical pathways. The AA. conclude that NMR is the choice examination in the evaluation of phakomatoses.</p>","PeriodicalId":76494,"journal":{"name":"Rivista di neurologia","volume":"60 3","pages":"96-101"},"PeriodicalIF":0.0000,"publicationDate":"1990-05-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Rivista di neurologia","FirstCategoryId":"1085","ListUrlMain":"","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 0

Abstract

23 patients affected by phakomatoses were studied with NMR, including tuberous sclerosis (11 cases), Sturge-Weber's disease and Von Recklinghausen's neurofibromatosis (6 cases). SE sequence was used performing T1-WIs with TR = 350-750 ms and TE = 20-30 ms and T2-WIs with TR = 1500-2100 ms and TE = 50-100 ms. Tuberous sclerosis was characterized in each case by the presence of hiperintense areas in T2-WIOs, associated in 9 cases to subependimal microcalcifications. Sturge-Weber-disease showed: cerebral or lobar emiatrophia, abnormal vascularization and cortical calcifications. Cerebral neurofibromatosis was characterized by extra-assial tumors, associated in 4 cases to gliomas of the optical pathways. The AA. conclude that NMR is the choice examination in the evaluation of phakomatoses.

分享 分享
微信好友 朋友圈 QQ好友 复制链接
本刊更多论文
[核磁共振的吞噬]。
采用核磁共振对23例吞噬病患者进行研究,其中结节性硬化症(11例)、Sturge-Weber病和Von Recklinghausen神经纤维瘤病(6例)。采用SE序列进行t1 - wi, TR = 350-750 ms, TE = 20-30 ms, t2 - wi, TR = 1500-2100 ms, TE = 50-100 ms。结节性硬化症的特点是在t2 - wio中存在高强度区域,其中9例与室管膜下微钙化有关。sturge - weber病表现为:大脑或大叶肌萎缩,血管化异常和皮质钙化。脑神经纤维瘤病以筋膜外肿瘤为特征,其中4例与视神经通路胶质瘤相关。AA。结论核磁共振是评价吞噬病的首选检查方法。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
求助全文
约1分钟内获得全文 去求助
来源期刊
自引率
0.00%
发文量
0
期刊最新文献
[Inflammatory myopathies]. Refsum's disease. Striated sphincter and genital dysfunctions in multiple sclerosis patients: an electrophysiological approach [Antiphospholipid antibodies and cerebral ischemia]. [Cerebrovascular manifestations while taking combined estrogens and progestins for contraceptive purposes. Clinical cases].
×
引用
GB/T 7714-2015
复制
MLA
复制
APA
复制
导出至
BibTeX EndNote RefMan NoteFirst NoteExpress
×
×
提示
您的信息不完整,为了账户安全,请先补充。
现在去补充
×
提示
您因"违规操作"
具体请查看互助需知
我知道了
×
提示
现在去查看 取消
×
提示
确定
0
微信
客服QQ
Book学术公众号 扫码关注我们
反馈
×
意见反馈
请填写您的意见或建议
请填写您的手机或邮箱
已复制链接
已复制链接
快去分享给好友吧!
我知道了
×
扫码分享
扫码分享
Book学术官方微信
Book学术文献互助
Book学术文献互助群
群 号:481959085
Book学术
文献互助 智能选刊 最新文献 互助须知 联系我们:info@booksci.cn
Book学术提供免费学术资源搜索服务,方便国内外学者检索中英文文献。致力于提供最便捷和优质的服务体验。
Copyright © 2023 Book学术 All rights reserved.
ghs 京公网安备 11010802042870号 京ICP备2023020795号-1