En coup de sabre linear scleroderma – diagnostic difficulties. Case report

Abstract

Frontal linear scleroderma (morphea en coup de sabre) is a rare disease from the group of limited connective tissue diseases, most often affecting children. Due to the fact that it is not a common dermatosis, diagnosis and treatment may be difficult. Therefore, we believe it is advisable to present the diagnostic difficulties in a patient of the Provincial Integrated Hospital in Elbląg. It is also noteworthy that the patient’s neurological symptoms preceded the appearance of skin lesions. Clinical symptoms and imaging studies led us to observe progressive hemifacial atrophy. The patient requires interdisciplinary specialist care and diagnosis in the field of neurology, dermatology, rheumatology and ophthalmology.