Left ventricular non-compaction with ventricular aneurysm in 6-year-old patient

Abstract

Ventricular noncompaction is a very rare form of cardiomyopathy and its combination with a ventricular aneurysm is even more uncommon. We present a clinical case of a 6-year-old girl, who was admitted to our clinic with complaints of physical exertion. Echocardiography demonstrated prominent trabeculations in the left ventricular wall with a lateral basal part ballooning out, findings consistent with noncompaction of the left ventricular myocardium with an aneurysm. Magnetic resonance imaging confirmed evidence of non-compacted myocardium with a non-compacted /compacted myocardium ratio of 2.7. Impaired left ventricular systolic function and left ventricular aneurysm with myocardial scarring were found on magnetic resonance imaging. Coronary angiography excluded coronary artery disease, which justified myocardial scarring due to microcirculatory disorder of non-compacted myocardium