Smriti Gupta, Sanjeev Handa, Debajyoti Chatterjee, Dipankar De, Rahul Mahajan
{"title":"Extensive Extragenital Lichen Sclerosus-Like Lesions in a Patient with Junctional Epidermolysis Bullosa","authors":"Smriti Gupta, Sanjeev Handa, Debajyoti Chatterjee, Dipankar De, Rahul Mahajan","doi":"10.4103/idoj.idoj_503_23","DOIUrl":null,"url":null,"abstract":"\n Epidermolysis bullosa (EB) is a heterogeneous group of genetic disorders characterized by the formation of blisters and/or at the sites of trauma. These heal with post-inflammatory hypopigmentation, scarring, or milia formation. We hereby present a child who presented with widespread hypopigmented atrophic areas, blistering at trauma-prone sites, and nail dystrophy. The significance of this particular case lies in the challenge of distinguishing between epidermolysis bullosa (EB) and bullous extragenital lichen sclerosus et atrophicus (LSA).","PeriodicalId":13335,"journal":{"name":"Indian Dermatology Online Journal","volume":null,"pages":null},"PeriodicalIF":1.9000,"publicationDate":"2024-07-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Indian Dermatology Online Journal","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.4103/idoj.idoj_503_23","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q3","JCRName":"DERMATOLOGY","Score":null,"Total":0}
引用次数: 0
Abstract
Epidermolysis bullosa (EB) is a heterogeneous group of genetic disorders characterized by the formation of blisters and/or at the sites of trauma. These heal with post-inflammatory hypopigmentation, scarring, or milia formation. We hereby present a child who presented with widespread hypopigmented atrophic areas, blistering at trauma-prone sites, and nail dystrophy. The significance of this particular case lies in the challenge of distinguishing between epidermolysis bullosa (EB) and bullous extragenital lichen sclerosus et atrophicus (LSA).