Bronchial Atresia with Eisenmenger Syndrome in a Complex Congenital Heart Disease-A Rare Coexistence: A Case Report.

Q3 Medicine The Journal of the Association of Physicians of India Pub Date : 2024-10-01 DOI:10.59556/japi.72.0693

Shruti Thakur, Sumala Kapila, Anupam Jhobta, Charu Smita Thakur

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Abstract

Background: Congenital bronchial atresia (CBA) is a relatively benign and uncommon pulmonary anomaly that is usually an incidental radiological finding. Bronchial atresia may also be acquired. Its association with pulmonary vascular anomalies and congenital heart disease (CHD) has been described in literature as a handful of case reports only.

Case description: We report a case of a 26-year-old female having a rare coexistence of bronchial atresia with a large patent ductus arteriosus (PDA) and a small atrial septal defect (ASD), and had Eisenmenger syndrome (ES) at the time of presentation. PDA itself causes pulmonary arterial hypertension (PAH) if not corrected early within a few months of infancy. On the contrary, CBA can also lead to PAH and along with PDA may have contributed to the development of ES in our case.

Conclusion: Timely diagnosis and treatment of CBA and its associated CHD may prevent or delay the complications occurring later on.

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患有复杂先天性心脏病的支气管闭锁与艾森曼格综合征--罕见的并存：病例报告。

背景：先天性支气管闭锁（CBA）是一种相对良性且不常见的肺部异常，通常是偶然的放射学发现。支气管闭锁也可能是后天形成的。其与肺血管异常和先天性心脏病（CHD）的关系在文献中仅有少量病例报告：我们报告了一例罕见的支气管闭锁与大动脉导管未闭（PDA）和小房间隔缺损（ASD）并存的 26 岁女性病例，该患者在发病时患有艾森曼格综合征（ES）。如果不在婴儿期几个月内及早纠正，PDA 本身会导致肺动脉高压（PAH）。相反，CBA 也会导致 PAH，在我们的病例中，CBA 可能与 PDA 一起导致 ES 的发生：结论：及时诊断和治疗 CBA 及其相关的先天性心脏病可预防或延缓日后发生的并发症。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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