Case Report of an Urgent Determination of Malignant Hyperthermia Status of a 24-Week Pregnant Patient Requiring Intrauterine Fetal Surgery.

IF 0.5 Q4 ANESTHESIOLOGY A&A practice Pub Date : 2024-12-05 eCollection Date: 2024-12-01 DOI:10.1213/XAA.0000000000001868
Maria D Tischer, David J Berman, Luke Michaelson, Erin A Tracy, Rachel E Bridwell, Angela M Curell
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Abstract

Malignant hyperthermia (MH) is a potentially fatal disorder triggered by volatile anesthetics or succinylcholine, inducing a hypermetabolic crisis in susceptible patients. The caffeine-halothane contracture test (CHCT) remains a gold standard for MH detection. The authors describe a pregnant patient with a history of exertional rhabdomyolysis, who required urgent MH screening for administration of MH-triggering anesthetics. This anesthetic plan allowed for an in utero myelomeningocele repair for a 24-week-old fetus. A multi-institutional team coordinated the urgent CHCT and repair with a favorable outcome.

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紧急确定恶性高热状态的24周妊娠患者需要宫内胎儿手术的病例报告。
恶性热疗(MH)是一种由挥发性麻醉剂或琥珀酰胆碱引发的潜在致命疾病,可诱发易感患者的高代谢危象。咖啡因-氟烷收缩试验(CHCT)仍然是MH检测的金标准。作者描述了一个有外力性横纹肌溶解病史的孕妇,她需要紧急MH筛查以使用MH触发麻醉剂。该麻醉方案允许对24周大的胎儿进行子宫内脊髓脊膜膨出修复。一个多机构团队协调了紧急CHCT和修复,并取得了良好的结果。
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来源期刊
A&A practice
A&A practice Medicine-Medicine (all)
CiteScore
1.40
自引率
0.00%
发文量
126
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