Rapidly Progressing Secondary Organizing Pneumonia in a Case of Systemic Sclerosis Sine Scleroderma - A Diagnostic Urgency: A Case Report and Literature Review.

Abstract

Systemic sclerosis sine (latin: without) scleroderma (ssSSc), also called visceral scleroderma, is characterized by internal organ involvement and abnormal serologic abnormalities in the complete or partial absence of cutaneous manifestations of systemic sclerosis.1,2 Pulmonary involvement in scleroderma consists of interstitial lung disease and pulmonary hypertension. Usual interstitial pneumonia (45.4%), followed by nonspecific interstitial pneumonia (36.4%) represents the predominant interstitial lung disease in scleroderma.3 Rarely, organizing pneumonia has been described with scleroderma and seldom with systemic sclerosis sine scleroderma in literature.