Congenital cranial fasciitis of the ethmoid bone with extensive intracranial and facial involvement: a case report and review of the literature

Abstract

Cranial fasciitis is a rare fibroproliferative condition predominantly affecting children. An unusual case of cranial fasciitis in a full-term male newborn presenting with significant right malar swelling is reported. Initial imaging revealed a large frontal extra-axial mass displacing both frontal lobes and extending to the right infratemporal fossa and orbit, subsequently diagnosed via a transoral biopsy. Two-stage surgery involving a multidisciplinary team was performed to completely remove both the intracranial and extracranial components of the lesion. Long-term follow-up MRI indicated no recurrence of the disease at 16 months post-resection. Multidisciplinary collaboration is crucial in managing complex craniofacial conditions, especially in newborns and infants.