{"title":"Myectomy-myotomy for long segment Hirschsprung's disease in a patient with Haddad syndrome","authors":"Iyore A. Otabor , Jane P. Balint , Gail E. Besner","doi":"10.1016/j.jpedsurg.2008.10.115","DOIUrl":null,"url":null,"abstract":"<div><p><span>Hirschsprung's disease<span> is a rare entity with an incidence of 1 in 5000 live born infants. Long segment Hirschsprung's disease occurs in approximately 5% to 10% of this patient population and is defined as a transition zone proximal to the sigmoid colon (Bodian M, Carter CO, Ward BC. Hirschsprung's disease. </span></span><em>Lancet</em><span>. 1951;1:302-309). The association of congenital central hypoventilation syndrome (also known as </span><em>Ondine's curse</em>) and Hirschsprung's disease is termed <em>Haddad syndrome</em>.</p></div>","PeriodicalId":16733,"journal":{"name":"Journal of pediatric surgery","volume":"44 3","pages":"Pages 620-622"},"PeriodicalIF":2.4000,"publicationDate":"2009-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1016/j.jpedsurg.2008.10.115","citationCount":"4","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Journal of pediatric surgery","FirstCategoryId":"3","ListUrlMain":"https://www.sciencedirect.com/science/article/pii/S0022346808009792","RegionNum":2,"RegionCategory":"医学","ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q1","JCRName":"PEDIATRICS","Score":null,"Total":0}
引用次数: 4
Abstract
Hirschsprung's disease is a rare entity with an incidence of 1 in 5000 live born infants. Long segment Hirschsprung's disease occurs in approximately 5% to 10% of this patient population and is defined as a transition zone proximal to the sigmoid colon (Bodian M, Carter CO, Ward BC. Hirschsprung's disease. Lancet. 1951;1:302-309). The association of congenital central hypoventilation syndrome (also known as Ondine's curse) and Hirschsprung's disease is termed Haddad syndrome.
先天性巨结肠病是一种罕见的疾病，其发病率为每5000个活产儿中有1个。长节段先天性巨结肠的发病率约为5% - 10%，定义为乙状结肠近端过渡区(Bodian M, Carter CO, Ward BC)。巨结肠病。《柳叶刀》杂志。1951;1:302 - 309)。先天性中枢性低通气综合征(也称为Ondine的诅咒)和先天性巨结肠病的关联被称为哈达德综合征。
期刊介绍：
The journal presents original contributions as well as a complete international abstracts section and other special departments to provide the most current source of information and references in pediatric surgery. The journal is based on the need to improve the surgical care of infants and children, not only through advances in physiology, pathology and surgical techniques, but also by attention to the unique emotional and physical needs of the young patient.
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