Josaphat Iba Ba, Jean Raymond Nzenze, Franck Moubamba, Angela Sonia Iroki Mboumba, Landry Missounga, Rufin Bignoumba Ibouili, Sophie Coniquet, Jean-Baptiste Moussavou Kombila, Jean Bruno Boguikouma
{"title":"[Still disease in subSaharan Africa: report of four cases in Gabon].","authors":"Josaphat Iba Ba, Jean Raymond Nzenze, Franck Moubamba, Angela Sonia Iroki Mboumba, Landry Missounga, Rufin Bignoumba Ibouili, Sophie Coniquet, Jean-Baptiste Moussavou Kombila, Jean Bruno Boguikouma","doi":"10.1684/san.2011.0241","DOIUrl":null,"url":null,"abstract":"<p><p>Still disease is an inflammatory rheumatism occurring predominantly in children and adolescents, but which is sometimes diagnosed in adults. A combination of fever, arthralgia, transient dermatological lesions, hyperleucocytosis predominantly neutrophilic, and ferritinaemia greater than 1,000 μg/L is suggestive of this disease, but infectious, haematological, immunological, and tumor diseases must first be ruled out. Accordingly, patients' financial limitations keep this disease from being diagnosed often in sub-Saharan Africa. We report four cases of Still disease with favourable outcome after corticosteroid therapy.</p>","PeriodicalId":79375,"journal":{"name":"Sante (Montrouge, France)","volume":"21 2","pages":"97-101"},"PeriodicalIF":0.0000,"publicationDate":"2011-04-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://sci-hub-pdf.com/10.1684/san.2011.0241","citationCount":"4","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Sante (Montrouge, France)","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.1684/san.2011.0241","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 4
Abstract
Still disease is an inflammatory rheumatism occurring predominantly in children and adolescents, but which is sometimes diagnosed in adults. A combination of fever, arthralgia, transient dermatological lesions, hyperleucocytosis predominantly neutrophilic, and ferritinaemia greater than 1,000 μg/L is suggestive of this disease, but infectious, haematological, immunological, and tumor diseases must first be ruled out. Accordingly, patients' financial limitations keep this disease from being diagnosed often in sub-Saharan Africa. We report four cases of Still disease with favourable outcome after corticosteroid therapy.