Loeys-Dietz syndrome.

Abstract

A 25-year-old man presented with abdominal pain. He was tall with arachnodactyly and hypermobile joints. Family history was unremarkable. CT angiogram revealed a descending aortic dissection extending superiorly from a 4.5 cm infrarenal abdominal aortic aneurysm (Figure 1). He was managed medically in the hospital and discharged with recommendations for close interval imaging. One month later he returned to the Emergency Department with chest pain. CT angiogram demonstrated proximal expansion of the dissection to the left subclavian artery (Figure 2). Woven vascular graft s were utilized to repair the thoracoabdominal