[A CASE OF COMPLETE RESECTION OF PROGRESSIVE RETROPERITONEAL LEIOMYOSARCOMA WITH INFERIOR VENA CAVA TUMOR THROMBUS AND LIVER METASTASIS].

Q4 Medicine Japanese Journal of Urology Pub Date : 2020-01-01 DOI:10.5980/jpnjurol.111.145
Yuma Kujime, Atsunari Kawashima, Nobuhiko Kawata, Kentaro Takezawa, Taigo Kato, Koji Hatano, Takeshi Ujike, Toyofumi Abe, Shinichiro Fukuhara, Kazutoshi Fujita, Motohide Uemura, Hiroshi Kiuchi, Ryoichi Imamura, Norio Nonomura
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Abstract

We present a case in a 74-year-old female patient whose initial symptom was right flank pain. Enhanced computed tomography showed a mass (about 15×12 cm) in the retroperitoneum, inferior vena cava tumor thrombus (Level III: Neves and Zincke system) and liver metastasis. The primary tumor exploded and inferior vena cava tumor thrombus caused congestive liver one and a half month later. Preoperative diagnosis was right adrenocortical carcinoma (cT4N0M1 stage IV). We performed complete resection of tumor including metastasis. Pathological findings on the resected specimen revealed pleomorphic leiomyosarcoma, which was discontinuous tumor from the right normal adrenal grand. There was no evidence of local recurrence or metastasis after 6 months with no additional treatment.

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【进行性腹膜后平滑肌肉瘤伴下腔静脉肿瘤血栓及肝转移全切除1例】。
我们提出一个病例在一个74岁的女性患者,其最初的症状是右侧疼痛。增强ct显示腹膜后肿块(约15×12 cm),下腔静脉肿瘤血栓(III级:Neves和Zincke系统)及肝脏转移。1个半月后原发肿瘤破裂,下腔静脉肿瘤血栓形成充血性肝。术前诊断为右侧肾上腺皮质癌(cT4N0M1期),行肿瘤全切及转移。切除标本的病理结果显示为多形性平滑肌肉瘤,这是一种来自右侧正常肾上腺的不连续肿瘤。6个月后未见局部复发或转移。
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来源期刊
Japanese Journal of Urology
Japanese Journal of Urology Medicine-Urology
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