Pancreatic paraganglioma: an extremely rare entity with unusual age presentation and uncommom site

Abstract

Introduction: Paraganglioma are rare neuroendocrine neoplasm, affecting about 1 in 2,000,000 populations, which arise in the extra-adrenal chromaffin cells of the autonomic nervous system. It is a generic term applied to all tumors of paraganglia regardless of the location. In rare instances, paragangliomas present around and involve the pancreas, thereby mimicking one of the common primary pancreatic lesions.