Special Patients: Epidermolysis Bullosa

Abstract

Background: Epidermolysis bullosa (EB) is a relatively rare hereditary dermatosis that has different clinical presentations and is characterized by the appearance of blisters on the skin and mucous membranes. Some forms of EB present stomatological manifestations, such as blisters on the palate, motor difficulties of the tongue, floor of the mouth, scars on the lips, in addition to dental dysplasias, microstomia and periodontal disease. Case description: In the present work, the author reviews the literature on the subject and present a clinical case of a 15-year-old patient with recessive dystrophic epidermolysis bullosa, focusing on the main stomatological manifestations of the disease.