Amadou Djibrilla-Almoustapha, M. Maman-Brah, Moustapha Elhadji-Chefou, M. R. Badé, Amal Al-Azhari, Youssoufa Seydou-Moussa, M. Sani, M. Daou, S. Brah, B. Malam-Abdou
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引用次数: 0
Abstract
Von Willebrand’s disease was first described in 1926 by Erik Von Willebrand. It is a genetic, constitutional defect of hemostasis that is different from hemophilia. It is classified among the rare diseases whose clinical manifestations are dominated by a hemorrhagic profile, which varies from patient to patient. It is an easily diagnosed disease based on a quantitative and qualitative bioassay of VWF. Treatment is multidisciplinary and is based on well-structured prevention. We report the first case of von Willebrand disease in Niger, diagnosed in the Hematology Department of Niamey’s National Hospital.
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