Melanotic Neuroectodermal Tumor of Infancy: A Case Report with Review of Literature

Vasundhara Patil, Jeba Nazneen, P. Rai, Ujjwal Agarwal, A. Mahajan
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Abstract

Abstract Melanotic neuroectodermal tumors of infancy are rare pigmented neuroectodermal locally aggressive tumors that usually occur within 1 year of life. Head and neck areas are frequently involved with maxilla being the most common site. Expansile growth and high recurrence rate are characteristics of this cancer. Though rare, radiologists and clinicians must be aware and should consider this entity when diagnosing pediatric head and neck masses. Computed tomography can be used for diagnosing and looking at the extent of the disease and predicting the operative outcome. Surgery with wide resection margin is the mainstay of treatment for these masses. Surgery followed by adjuvant chemotherapy and radiation is reserved for aggressive malignant lesions. Since it has a high recurrence rate, follow-up is done with imaging and clinical examination. Early detection and treatment of recurrence have a favorable outcome for the patients.
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婴儿期黑色素样神经外胚层肿瘤1例并文献复习
婴儿期黑色素神经外胚层肿瘤是一种罕见的色素性神经外胚层局部侵袭性肿瘤,通常发生在1岁以内。头部和颈部经常受累,上颌骨是最常见的部位。扩张性生长和高复发率是这种癌症的特点。虽然罕见,放射科医生和临床医生必须意识到,并应考虑到这个实体诊断儿童头颈部肿块。计算机断层扫描可用于诊断和观察疾病的程度,并预测手术结果。广泛切除的手术是治疗这些肿块的主要方法。手术后的辅助化疗和放疗是为侵略性恶性病变保留的。由于复发率高,随访需进行影像学和临床检查。早期发现和治疗复发对患者有良好的效果。
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来源期刊
CiteScore
0.40
自引率
0.00%
发文量
91
期刊介绍: The journal will cover technical and clinical studies related to medical and pediatric oncology in human well being including ethical and social issues. Articles with clinical interest and implications will be given preference.
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