Management of Two Years Old Child with Russell-Silver Syndrome - A Case Report

Abstract

Russell-Silver syndrome (RSS) is a rare genetic malformation characterized by the growth of a 2-year-old male child with RSS who underwent hip spica surgery under general anesthesia. The patient had a history of mild developmental delay, failure to gain weight, and frequent vomiting. Anesthetic implications of RSS, including airway management, glucose homeostasis, hypothermia, and pharmacological considerations, were considered during the patient's pre-operative assessment and intraoperative management. The patient was induced with propofol and fentanyl, and maintenance anesthesia was achieved with sevoflurane. The patient's airway was safely secured, and extubation was performed smoothly. The anesthetic management proceeded without complications, ensuring a successful outcome. This case report highlights the importance of considering the specific anesthetic implications of RSS in the perioperative management of patients with this rare genetic syndrome.