A Rare Case of Exclusively Extragenital Lichen Sclerosus in a Child

Abstract

Background. Lichen sclerosus (LS) is a chronic, inflammatory skin condition of unknown etiology that shows a predilec-tion for the anogenital region. Although LS primarily affects postmenopausal women, some cases do occur in children. However, in the pediatric setting, LS almost always affects the anogenital region with exclusively extragenital involvement very rarely diagnosed in childhood. Here, we present a 6-year-old girl with a 2-year history of thin, pink macules and plaques on her chest and back, which biopsy revealed to be extragenital LS. A review of this case and the literature describes the epidemiology, clinical features, pathophysiology, and treatment options for pediatric extragenital LS.