Takayasu Arteritis Presenting as Severe Pulmonary Hypertension

R. Bhardwaj, Ranjana Gupta, Sivaji Patibandla, Himanshu Tanwar, M. Ahmed, Gaurav Aggrawal
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Abstract

Takayasu arteritis is an inflammatory disease of large- and medium-sized arteries, with a predilection for the aorta and its branches. Advanced lesions demonstrate a panarteritis with intimal proliferation. It can affect the aorta, subclavian artery, renal artery, iliac artery, coronary artery, and other blood vessels. Pulmonary arteritis is very uncommon in TA. We describe a case of TA, who primarily presented with pulmonary hypertension.
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高须动脉炎表现为严重肺动脉高压
高松动脉炎是一种大中型动脉的炎症性疾病,以主动脉及其分支为主。晚期病变表现为泛动脉炎伴内膜增生。可累及主动脉、锁骨下动脉、肾动脉、髂动脉、冠状动脉等血管。肺动脉炎在TA中很少见。我们描述了一个主要表现为肺动脉高压的TA病例。
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