Cavernous Lymphangioma of the Digits: A Rare Cause of Macrodactyly

Abstract

MATERIALS & METHODS: An 18-month-old girl presented with a gradually enlarging bulbous swelling of the left ring and little finger since birth. Both fingers were swollen and sausage like with marked ulna deviation of the distal phalanges. The swellings were asymmetrical, soft, smooth and multilobulated extending over the dorsum of the hand from the metacarpophalangeal joints till the distal interphalangeal joints (Figure 1) and compromised the function of both digits. Radiograph showed a large soft tissue shadow with no bony involvement. MRI revealed a large subcutaneous tissue mass of the ring and little fingers with no definite margins. The mass was homogenous in consistency, hypointense in T1 and hyperintense in T2 weighted sequence indicating presence of fat. The provisonal diagnosis was macrodystrophic lipomatosa of the ulnar nerve as the bones were normal in size and the nonfatty dominance of the mass atypical of such lesion. She then underwent two debulking surgeries.