Budd Chiari Syndrome in a Fifteen-Year Old Girl with Systemic Lupus Erythematosus

Abstract

Budd Chiari Syndrome is a rare disease that results from the complication of venous thrombosis. In this case report, the syndrome is being reported in a 15 year old young Pakistani girl first diagnosed with Systemic Lupus Erythematosus (SLE) two years earlier. She was one of those on a one year regular follow-up in the Rheumatology Department of Fatimah Memorial Hospital, Lahore, Pakistan. It is believed that in this patient, Budd Chiari Syndrome resulted from hepatic veinous thrombosis due to the presence of Lupus anticoagulants. As the young girl was suffering from antiphospholipid syndrome secondary to lupus, this milder form of Budd-Chiari Syndrome was later treated in India with surgical shunts. Keywords: Systemic lupus erythematosus; Budd-Chiari Syndrome; lupus anticoagulants; thrombosis; antiphospholipid syndrome.