Anomalous portal branches associated with polysplenia syndrome: imaging findings

Abstract

We report on a 65-year-old man with anomalous portal venous branches associated with azygos continuation and polysplenia syndrome. Ultrasound and CT of the upper abdomen demonstrated a preduodenal portal vein with stenotic intrahepatic portal venous branches; the portal blood mainly flowed into the right anterior portal branch via the preduodenal portal vein, with several accessory portal branches that flowed directly into the hepatic segments VI and III. Portal venous anomalies with such multiple accessory branches have not been reported previously.