{"title":"Lamellar Ichthyosis; An Uncommon Acquaintance with Anesthesiologists: Overcoming Barriers","authors":"Ravichandran Narayanan, S. Patil, Raghuvarathan","doi":"10.4103/2394-6954.227080","DOIUrl":null,"url":null,"abstract":"Lamellar ichthyosis constitutes a distinct group of inherited ichthyosis characterized by excessive scaling and dryness. Abnormalities in epidermal differentiation and metabolism contribute to excessive keratinization, which is a hallmark of this disorder. We present here the successful anesthetic management of a 13-year-old boy with lamellar ichthyosis for the correction of Genu Valgum deformity.","PeriodicalId":17751,"journal":{"name":"Karnataka Anaesthesia Journal","volume":"3 1","pages":"6 - 9"},"PeriodicalIF":0.0000,"publicationDate":"2017-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"1","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Karnataka Anaesthesia Journal","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.4103/2394-6954.227080","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 1
Abstract
Lamellar ichthyosis constitutes a distinct group of inherited ichthyosis characterized by excessive scaling and dryness. Abnormalities in epidermal differentiation and metabolism contribute to excessive keratinization, which is a hallmark of this disorder. We present here the successful anesthetic management of a 13-year-old boy with lamellar ichthyosis for the correction of Genu Valgum deformity.