Surgical Management of Inguinal Hernia in a Newborn with ARCL2B

Abstract

world with an incidence of 1 in 1 million and is equally distributed in both sexes.1 It may be congenital or acquired. It affects connective tissue that supports the body’s framework which provides structure and strength to the muscles, joints, organs, and skin. The underlying pathology is related with elastin fibers. It results in skin manifestations such as the aged face, loose redundant skin, and reduced elasticity; and extracutaneous manifestations such as diverticula at the gastrointestinal system or urinary system, gastroesophageal reflux, diaphragmatic atonia or a hernia, umbilical or an inguinal hernia and hypoplasia of corpus callosum.2-4 In the literature, there are many reports about cutis laxa and its comorbidities but none is related with per operative management of the patient. To our knowledge, this will be the first case that discusses the surgical management of an autosomal recessive cutis laxa (ARCL2B) patient in English literature.