Isolated Right Ventricular Non-compaction in a Neonate with Gestational Diabetes Mother: a case report

Abstract

Background: An arrest in normal endomyocardial embryogenesis results in ventricular non - compaction which is a rare congenital cardiomyopathy. Non-compaction of the ventricular myocardium is a rare cardiomyopathy characterized by a pattern of prominent trabecular meshwork and deep inter-trabecular recesses. The clinical manifestation includes systolic and diastolic dysfunction, heart failure, ventricular arrhythmias and cardio embolic events.Case report: We describe neonate gestational diabetes mother (GDM) (38 weeks, weight of 2580 gr) with isolated right ventricular non-compaction and systolic and diastolic right heart dysfunction and according to meconium aspiration syndrome and complication with tension pneumothorax. Follow up after Six month showed total improving spontaneously. Conclusion: It is important to consider RVNC cardiomyopathy as a differential diagnosis cyanosis and respiratory distress at meconium aspiration syndrome in a neonate deliver from a GDM. Also despite RV cardiac dysfunction RVNC can tolerance complication such as pulmonary hypertension and tension pneumothorax, however with stand RV preload and afterload. At the end, RVNC in GMD could be improving spontaneously.