Primary Cardiac Rhabdomyosarcoma in a Child—A Case Report

K. Maram, V. Kudumula, Dilip Ratti, Sindhura Paturi
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Abstract

Unlike benign primary cardiac tumors like rhabdomyomas and fibromas, primary malignant tumors are extremely rare in children with very few cases reports in the literature so far. Rhabdomyosarcoma is a rare primary malignant tumor in children with most reported cases occurring in the right heart. We report a 15-month-old child with a primary rhabdomyosarcoma arising from the left ventricle and presenting with cardiac tamponade and circulatory failure. He underwent a diagnostic sternotomy and palliative chemotherapy but succumb to the disease later.
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儿童原发性心脏横纹肌肉瘤1例报告
与横纹肌瘤、纤维瘤等良性原发性心脏肿瘤不同,原发性恶性肿瘤在儿童中极为罕见,目前文献报道的病例很少。横纹肌肉瘤是一种罕见的儿童原发性恶性肿瘤,大多数报告病例发生在右心脏。我们报告一个15个月大的儿童原发性横纹肌肉瘤起源于左心室,并表现为心脏填塞和循环衰竭。他接受了诊断性胸骨切开术和姑息性化疗,但后来死于疾病。
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